Two Cases of Restrictive Cardiomyopathy in Children
نویسندگان
چکیده
منابع مشابه
[Two cases of idiopathic restrictive cardiomyopathy].
概 要 拘 束型心 筋症は ア ミロイ ドーシ スな どに伴 うものが多 く,特 発性 の もの は まれ であ る. 今回我 々は特発性 の2例 を経 験 した.心 臓 カテ ーテル検 査な どでは収縮性 心膜炎 に類似 した病 態がみ られたた め心膜切除 術 を施 行 した.症 例1. 31才,女 性.17才 よ り息 切れ が出現 し,21才 時MSと して交連切 開術 を受けて いる,心 エ コー図上,心 膜の肥厚 を認め た.症 例2. 46才,女 性.1年 前 よ り心 膜液貯留 と右心不 全症状 が出現 した.心 臓 カテ ーテ ル検 査で は両例 ともに右 心室拡張 寒期圧 の上昇 を認 め,左 右 の心室圧 は拡張期 はほぼ 等 しく,圧 波形 はdip and plateau を呈 した.術 中所 見で は2例 とも心膜 の肥厚,癒 着は軽度 であつ た.術 後...
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متن کاملRestrictive Cardiomyopathy
Restrictive cardiomyopathy (RCM) is a myocardial disorder that usually results from increased myocardial stiffness that leads to impaired ventricular filling. Biventricular chamber size and systolic function are usually normal or nearnormal until later stages of the disease. Affecting either or both ventricles, RCM may cause signs or symptoms of left or right heart failure. Arrhythmias and cond...
متن کاملElectrocardiographic and clinical characteristics of idiopathic restrictive cardiomyopathy in children.
BACKGROUND Idiopathic restrictive cardiomyopathy (RCM) is not a single disease and is rare. METHODS AND RESULTS The clinical features and clinical course of 12 pediatric patients with RCM seen between 1978 and 2005 were retrospectively analyzed. The age at diagnosis ranged from 4 months to 12 years (median 4 years). The age of 7 patients diagnosed because of an abnormal electrocardiogram (ECG...
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Background and aim: Tachyx is a rare autosomal recessive and neurological disorder caused by glycosfenolipid accumulation (GM2 ganglioside) in cell lysosomes. The accumulation of GM2 ganglioside is due to the mutation in the beta-hexose aminase gene (HEXA), which reduces the activity and deficiency of the HEXA enzyme. The aim of this study was to report 2 cases of T.Sax disease. Case report:...
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ژورنال
عنوان ژورنال: Journal of Nippon Medical School
سال: 2009
ISSN: 1345-4676,1347-3409
DOI: 10.1272/jnms.76.313